Acute exacerbations of progressive-fibrosing interstitial lung diseases
Acute exacerbation of interstitial lung disease (ILD) is associated with a poor prognosis and high mortality.Numerous studies have documented acute exacerbation in idiopathic pulmonary fibrosis (IPF), but less is known about these events in other ILDs that may present a progressive-fibrosing phenotype.We propose defining acute exacerbation as an ac